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Interstitial lung disease in infancy: A general approach

Identifieur interne : 000E07 ( Main/Exploration ); précédent : 000E06; suivant : 000E08

Interstitial lung disease in infancy: A general approach

Auteurs : Erica J. Hines [Australie] ; Mark Walsh [Australie] ; Jane E. Armes [Australie] ; Tonia Douglas [Australie] ; Jasneek Chawla [Australie]

Source :

RBID : ISTEX:2DC26ACD7C857FC7999D0411A0A142E49DF24DA4

Abstract

Childhood Interstitial lung disease (chILD) is an umbrella term used to define a broad range of rare, diffuse pulmonary disorders with altered interstitial structure that leads to abnormal gas exchange. Presentation of chILD in infancy can be difficult to differentiate from other common causes of diffuse lung disease. This article aimed at paediatricians provides an overview of interstitial lung disease presenting in infancy and includes key clinical features, a suggested approach to investigation and a summary of management. An overview of three clinical cases has been included to demonstrate the diagnostic approach, characteristic investigation findings and varied clinical outcomes.

Url:
DOI: 10.1111/jpc.13162


Affiliations:


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Le document en format XML

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<div type="abstract">Childhood Interstitial lung disease (chILD) is an umbrella term used to define a broad range of rare, diffuse pulmonary disorders with altered interstitial structure that leads to abnormal gas exchange. Presentation of chILD in infancy can be difficult to differentiate from other common causes of diffuse lung disease. This article aimed at paediatricians provides an overview of interstitial lung disease presenting in infancy and includes key clinical features, a suggested approach to investigation and a summary of management. An overview of three clinical cases has been included to demonstrate the diagnostic approach, characteristic investigation findings and varied clinical outcomes.</div>
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